Woolly Hair Nevus Associated With an Ipsilateral Linear Epidermal Nevus

Martín-González, T.; del Boz-González, J.; Vera-Casaño, A.

doi:10.1016/S1578-2190(07)70426-2

Actas Dermo-Sifiliográficas

ISSN: 0001-7310

The Official publication of the Spanish Academy of Dermatology and Venereology (AEDV). Actas Dermo-Sifiliográficas, founded in 1909, is the oldest monthly medical journals published in Spain. In the year 2006 has been indexed in the Medlinedatabase, and has become a vehicle for expressing the most current Spanish medicine and modern. All articles are subjected to a rigorous process of revision in pairs, and careful editing for literary and scientific style. Together with the classic Original and Clinical Case Study sections, we also include Reviews, Case Diagnoses, and Book Reviews. Dermo-Sifiliográficas is an essential publication for anyone who needs to be current on all aspects of Spanish and world dermatology.

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We report a 4-year-old boy with two areas of woolly hair in the right parietotemporal region and a linear epidermal nevus in the areas of woolly hair as well as in the ipsilateral hemiface and chin. Evaluation by scanning electron microscopy showed woolly hair with oval transverse section and longitudinal groove. A complete examination ruled out associated anomalies.

Key words:

woolly hair

woolly hair nevus

lineal epidermis nevus

Resumen

Presentamos un paciente varón de 4 años con dos áreas de pelo lanoso en zona parietotemporal derecha y un nevus epidérmico lineal en las zonas de pelo lanoso, así como en hemicara y mentón ipsilateral. La imagen de microscopía electrónica de barrido mostraba el pelo lanoso con sección transversal oval y acanaladura longitudinal.

El estudio sistémico para descartar anomalías asociadas fue normal.

Palabras clave:

pelo lanoso

nevus de pelo lanoso

nevus epidérmico lineal

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