Journal Information
Vol. 98. Issue 9.
Pages 624-626 (November 2007)
Vol. 98. Issue 9.
Pages 624-626 (November 2007)
Case reports
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Becker Nevus Syndrome
Síndrome del Nevo de Becker
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A. Alfaroa, A. Tórreloa,
, Á. Hernándeza, A. Zambranoa, R. Happleb
a Servicio de Dermatología, Hospital del Niño Jesús, Madrid, Spain
b Servicio de Dermatología, Philipp University of Marburg, Marburg, Germany
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Abstract

Becker nevus is a hyperpigmented hamartoma with an irregular outline and often hairy. It is normally found on the shoulders and chest, although it can appear in other areas. Becker nevus is sometimes associated with other muscular, skeletal, or cutaneous abnormalities such as ipsilateral breast hypoplasia or scoliosis. This characteristic phenotype of Becker nevus associated with unilateral breast hypoplasia or other abnormalities is referred to as Becker nevus syndrome. Although the lesions usually become apparent during adolescence, they are present from birth and represent part of the spectrum of so-called epidermal nevus syndromes. We present 4 cases of Becker nevus syndrome in which Becker nevus was associated with ipsilateral breast hypoplasia and, less consistently, other abnormalities.

Key words:
Becker nevus
Becker nevus syndrome
breast hypoplasia
epidermal nevus
Resumen

El nevo de Becker es un hamartoma hiperpigmentado, de bordes geográficos y a menudo con hipertricosis en superficie. Sus localizaciones habituales suelen ser los hombros o el tórax, aunque puede aparecer en cualquier otra ubicación. En ocasiones el nevo de Becker se asocia a diferentes anomalías musculares, esqueléticas o cutáneas como la hipoplasia ipsilateral de la mama o la escoliosis. A este fenotipo característico de nevo de Becker asociado a hipoplasia unilateral de la mama u otras anomalías se le denomina síndrome del nevo de Becker. Aunque las lesiones suelen manifestarse en la adolescencia, éstas están presentes desde el nacimiento y constituyen una parte del espectro de los llamados síndromes de nevo epidérmico.

Presentamos 4 casos de síndrome del nevo de Becker, en el que el nevo de Becker se asoció a hipoplasia mamaria ipsilateral y, menos consistentemente, a otras anomalías.

Palabras clave:
nevo de Becker
síndrome del nevo de Becker
hipoplasia mamaria
nevo epidérmico
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Copyright © 2007. Academia Española de Dermatología y Venereología and Elsevier España, S.L.
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